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Preview	Issue Date	Title	Author(s)
	2004	Mutational analysis of mucopolysaccharidosis type VI patients undergoing a trial of enzyme replacement therapy	Karageorgos, L.; Harmatz, P.; Simon, J.; Pollard, A.; Clements, P.; Brooks, D.; Hopwood, J.
	2004	Identification and molecular characterization of α-L-iduronidase mutations present in mucopolysaccharidosis type I patients undergoing enzyme replacement therapy	Yogalingam, G.; Guo, X.; Muller, V.; Brooks, D.; Clements, P.; Kakkis, E.; Hopwood, J.
	2001	Gentamicin-mediated suppression of Hurler syndrome stop mutations restores a low level of a-L-iduronidase activity and reduces lysosomal glycosaminoglycan accumulation	Keeling, K.; Brooks, D.; Hopwood, J.; Li, P.; Thompson, J.; Bedwell, D.
	1995	In vivo delivery of human α-L-iduronidase in mice implanted with neo-organs	Salvetti, A.; Moullier, P.; Cornet, V.; Brooks, D.; Hopwood, J.; Danos, O.; Heard, J.M.
	2005	Prediction of neuropathology in mucopolysaccharidosis I patients	Fuller, M.; Brooks, D.; Evangelista, M.; Hein, L.; Hopwood, J.; Meikle, P.
	1998	Genotype-phenotype correlations in mucopolysaccharidosis type I using enzyme kinetics, immunoquantification and in vitro turnover studies	Bunge, S.; Clements, P.; Byers, S.; Kleijer, W.; Brooks, D.; Hopwood, J.
	1997	Lysosomal biogenesis in lysosomal storage disorders	Karageorgos, L.; Isaac, E.; Brooks, D.; Ravenscroft, E.; Davey, R.; Hopwood, J.; Meikle, P.
	1999	Altered trafficking and turnover of LAMP-1 in Pompe disease-affected cells	Meikle, P.; Yan, M.; Ravenscroft, E.; Isaac, E.; Hopwood, J.; Brooks, D.
	2000	Regulation of the lysosome-associated membrane protein in a sucrose model of lysosomal storage	Isaac, E.; Karageorgos, L.; Brooks, D.; Hopwood, J.; Meikle, P.